MIDAORTIC SYNDROME IN A 4-YEAR OLD BOY – A CASE REPORT

  • Mojca Zajc Avramovič Pediatric clinic, Unicersity clinical center Ljubljana
  • Rina Rus Clinical department of Nephrology, Pediatric clinic, University clinical centre Ljubljana
DOI: https://doi.org/10.6016/ZdravVestn.1175
Keywords: aortic disease, hypertension, hypertension therapy, abdominal aorta, vascular surgical procedures

Abstract

Middle aortic syndrome (MAS) is a rare clinical condition defined by segmental narrowing of lower thoracic aorta or abdominal aorta and her branches. The most common clinical manifestation is severe hypertension, it can also manifest as abdominal or lower-limb claudication. Untreated patients have greatly shortened life expectancy. Diagnosis is made by angiography. Treatment consists of surgical correction and antihypertensive medications.

We present a case of a 4-year old boy with MAS, who is treated at Department of Pediatric Nephrology in University Children's Hospital in Ljubljana.

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Author Biographies

Mojca Zajc Avramovič, Pediatric clinic, Unicersity clinical center Ljubljana
Pediatric resident
Rina Rus, Clinical department of Nephrology, Pediatric clinic, University clinical centre Ljubljana

doc. dr. Rina Rus, dr.med.

Clinical department of Nephrology, Pediatric clinic, University clinical centre Ljubljana

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Published
2015-04-07
How to Cite
1.
Zajc Avramovič M, Rus R. MIDAORTIC SYNDROME IN A 4-YEAR OLD BOY – A CASE REPORT. TEST ZdravVestn [Internet]. 7Apr.2015 [cited 2May2024];84(2). Available from: http://vestnik-dev.szd.si/index.php/ZdravVest/article/view/1175
Issue
Vol 84 No 2 (2015): February
Section
Case report, short scientific article


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