HENOCH-SCHÖNLEIN PURPURA WITH AN ATYPICAL PRESENTATION OF THE DISEASE – presentation of three case reports and review of the current literature
Abstract
Background: Henoch-Schönlein purpura is the most common vasculitis of small blood vessels in children. The diagnosis of the disease is confirmed in a patient with a specific rash, joint inflamation, abdominal pain or renal disease. The specific rash is necesary for the confirmation of the diagnosis. Henoch-Schönlein purpura can rarely present with a complication withot a prior presentation of the rash. In these cases diagnosis is difficult until the presentation of the specific skin manifestation. In the majority of patients the disease course is not complicated and has a good prognosis.
Conclusion: In this article we present three patients with an atypical presentation of the disease and a review of current literature on the topic.
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References
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