ORAL CAVITY CHANGES IN PATIENTS WITH DYSOSTOSIS CLEIDOCRANIALIS – CASE REPORT

  • Matjaž Rode ZD Ljubljana Moste Prvomajska 5 1000 Ljubljana
  • Ignac Groznik ZD Ljubljana Moste Prvomajska 5 1000 Ljubljana
  • Mirela Kogoj Rode Stomatološka klinika Klinični center Zaloška 2 1525 Ljubljana
Keywords: dysostosis cleidocranialis, oral cavity changes, rehabilitation

Abstract

Background. Dysostosis cleidocranialis (DCC) is a rare systemic disease that can be classified as autosomaldominant hereditary dysplasia and presents with disease characteristical changes in mouth. These can cause severe psychological problems especially in adolescent patients.

Conclusions. Orthodontic treatment of the facial sceletal and teeth abnormalities can be problematic in patients with DCC. Therefore, interdisciplinary planned dental/orthodontic rehabilitation is vital. This article presents a rehabilitation method in female patient with DCC.

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How to Cite
1.
Rode M, Groznik I, Kogoj Rode M. ORAL CAVITY CHANGES IN PATIENTS WITH DYSOSTOSIS CLEIDOCRANIALIS – CASE REPORT. TEST ZdravVestn [Internet]. 1 [cited 5Aug.2024];73(11). Available from: http://vestnik-dev.szd.si/index.php/ZdravVest/article/view/2374
Section
Professional Article