PRIMARY FIBROSARCOMA OF THE HEART
Abstract
Background. Primary tumors of the heart are rare, with an incidence between 0.0017 and 0.27% in reported or collected autopsy series. Near 30% of primary tumors are malignant, among them sarcomas are most frequent. Clinical symptoms are nonspecific: signs of congestive heart failure, chest pain, cough, weakness. Echocardiography is still cornerstone of noninvasive detection of cardiac tumors; other diagnostic techniques are computerized axial tomography and nuclear magnetic resonance. Surgical resection of tumor is the most important way of the treatment of primary malignant cardiac tumors.
Conclusions. In this case report authors describe a 55 years old man with echocardiographicaly diagnosed cardiac tumor. Later, tumor was more precisely assessed by computerized tomography and nuclear magnetic resonance. Because of progression of the tumor and involvement of coronary vessels, the tumor was not suitable for surgical resection. At autopsy, a primary fibrosarcoma of the heart was confirmed.
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References
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