National reccomendations for the management of patients with haemophilia

  • Majda Benedik Dolničar Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana
  • Barbara Faganel Kotnik Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana
  • Lidija Kitanovski Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana
  • Irena Preložnik Zupan Klinični oddelek za hematologijo, Interna klinika, Univerzitetni klinični center Ljubljana
  • Saša Anžej Doma Klinični oddelek za hematologijo, Interna klinika, Univerzitetni klinični center Ljubljana
  • Maruša Debeljak Služba za specialno laboratorijsko diagnostiko, Pediatrična klinika, Univerzitetni klinični center Ljubljana
  • Tadej Pajič Specializiran hematološki laboratorij KO za hematologijo, Interna klinika, Univerzitetni klinični center Ljubljana
  • Janez Jazbec Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana
  • Petra Dovč Oddelek za rehabilitacijo, Ortopedska klinika, Univerzitetni klinični center Ljubljana
  • Tanja Tomaževič Center za otroško in preventivno zobozdravstvo, Stomatološka klinika, Univerzitetni klinični center Ljubljana
  • Mojca Matičič Klinika za infekcijske bolezni in vročinska stanja, Univerzitetni klinični center Ljubljana
  • Janez Tomažič Klinika za infekcijske bolezni in vročinska stanja, Univerzitetni klinični center Ljubljana
  • Nataša Tul Mandić Klinični oddelek za perinatologijo, Ginekološka klinika, Univerzitetni klinični center Ljubljana
  • Alenka Trampuš Bakija Služba za specialno laboratorijsko diagnostiko, Pediatrična klinika, Univerzitetni klinični center Ljubljana
Keywords: haemophilia, recommendations, comprehensive treatment, tertiary level competence, complications

Abstract

The document presents recommendations for the comprehensive treatment of patients with haemophilia in Slovenia. It enables health workers at all three levels of health care to become well-acquainted with all the possible aspects of treatment based on the best practices of major centres worldwide, and on the studies and experience of health professionals at the National Haemophilia Centre, University Medical Center Ljubljana. The document contains definitions, treatment algorithms and lists of medications with their characteristics and appropriate dosages. It specifically defines indications for the exclusive competence of the tertiary level in Ljubljana due to the actual availability of teams and laboratory options. It also contains an extensive list of the literature on haemophilia.

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Published
2017-11-06
How to Cite
1.
Benedik Dolničar M, Faganel Kotnik B, Kitanovski L, Preložnik Zupan I, Anžej Doma S, Debeljak M, Pajič T, Jazbec J, Dovč P, Tomaževič T, Matičič M, Tomažič J, Tul Mandić N, Trampuš Bakija A. National reccomendations for the management of patients with haemophilia. TEST ZdravVestn [Internet]. 6Nov.2017 [cited 19Apr.2024];86(9-10):422-78. Available from: http://vestnik-dev.szd.si/index.php/ZdravVest/article/view/2626
Section
Professional Article